Congenitally corrected transposition of great arteries (ccTGA) is a relatively rare cardiopathy, occurring in 1 case in 33 000 live births. It is rarely isolated and is often associated with other anomalies such as ventricular septal defects (80% cases), tricuspid valve anomalies (70% cases), pulmonary tract obstructions (30–50% cases), and sub aortic tract obstructions (rarely). However, association with coarctation of the aorta remains fairly rare, with prevalence poorly defined in the literature. Conduction disorders are frequent due to the existence of two AV nodes, with an annual risk of AVB of 2%.

To describe a clinical case associating ccTGA with a coarctation of the aorta revealed by a complete AV block.

The AV block and coarctation of aorta were considered to be the two main factors in systemic ventricular dysfunction.

It was decided to implant the patient with ventricular resynchronization (CRT-P), while the coarctation of the aorta was treated percutaneously.

Systemic ventricular failure should raise the suspicion of pressure overload, such as coarctation of the aorta. Early removal of the obstruction can delay deterioration of the contractile function of the systemic ventricle.

The authors have not supplied their declaration of competing interest.

Copyright © 2023 Published by Elsevier Masson SAS