Spinal hemangioblastomas (HBs) are rich vascular entities with a benign nature that comprise about 2%–6% of spinal tumors [1], [2]. They may be acompanied by von Hippel‒Lindau (VHL) syndrome or present in isolation form [1], [3], [4]. HBs usually affect cervical or thoracic segments and mainly occur intramedullary or intradural and extramedullary [1], [3], [5].

HBs involving the cauda equina are rarely encountered, with only 24 sporadic cases that commonly presented in the pattern of case reports [6], [7], [8], [9], [10], [11], [12], [13], [14]. These rare vascular lesions are usually preoperatively misinterpreted as ependymoma, neurofibroma, schwannoma [6], [9], [13], [15], [16], or other vascular lesions, such as capillary hemangiomas or cavernous malformations [17]. Data on the clinical-radiological characteristics and long-term treatment results of patients with cauda equina HBs in a single-center series are still lacking due to their rarity. Therefore, this study was conducted to summarize the characteristics of cauda equina HBs to enhance our knowledge of this rare disease.