Case Report Revisiting Rosai Dorfman disease: A rare histiocytic disorder with nodal and extranodal involvement

Smily Sharma, Poonam Sherwani, Venkata S. Arunachalam, Rahul Dev

About the author(s) Smily Sharma, Department of Diagnostic and Interventional Radiology, All India Institutes of Medical Sciences (AIIMS) Jodhpur, Jodhpur, India
Poonam Sherwani, Department of Radiodiagnosis, All India Institutes of Medical Sciences (AIIMS) Rishikesh, Rishikesh, India
Venkata S. Arunachalam, Department of Imaging Sciences and Interventional Radiology, Sree Chitra Tirunal Institute for Medical Sciences and Technology, Thiruvananthapuram, India
Rahul Dev, Department of Radiodiagnosis, All India Institutes of Medical Sciences (AIIMS) Rishikesh, Rishikesh, India

Rosai Dorfman disease is a rare but benign and self-limiting disorder. A case of Rosai Dorfman disease in a 16-year-old female with classic radiological and pathological findings is presented. T2W hypointense signal of the soft tissue masses was a distinguishing MRI feature.

Contribution: Rosai Dorfman disease is often overlooked in the differentials of lymphadenopathy and soft tissue masses on account of its rarity. This case report comprehensively discusses the imaging approach to this rare disorder.

Rosai Dorfman disease; emperipolesis; massive lymphadenopathy; sinus histiocytosis; histiocytosis.

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