Noonan syndrome, an autosomal dominant disease known as a RASopathy, is caused by germline mutations in RAS-MAPK pathway genes such as PTPN11, SOS1, RAF1, RIT1, KRAS, BRAF, NRAS, SHOC2, and CBL [4]. Between 25 % and 40 % of patients exhibit dermatologic findings such as lymphedema, short curly hair, dystrophic nails, a tendency toward keloid formation, soft elastic skin, keratosis pilaris atrophicans, and abnormal dermatoglyphics [5]. Lymphedema is a concomitant manifestation in 20 % of